What is foregut duplication cyst?
What is foregut duplication cyst?
Background: Foregut duplications are rare entities that include both esophageal and bronchogenic cysts. The diagnosis of foregut duplication cyst is made most often from an incidental finding on chest radiograph, or due to respiratory compromise due to mass effect or infection. Treatment consists of complete resection.
Can a duplication cyst be cancerous?
Malignant transformation in isolated duplication cysts is extremely rare. Here we reported a resected case of advanced cancer arising from an isolated enteric duplication cyst surrounding the pancreas that initially diagnosed a mucinous cystic neoplasm (MCN).
What is a duplication cyst?
Enteric duplication cysts, sometimes simply called duplication cysts, are rare congenital malformations of the gastrointestinal tract. They most frequently occur in the small intestine, particularly the ileum, but can occur anywhere along the gastrointestinal tract. They may be cystic or tubular in conformation.
What is a foregut cyst?
Foregut (Bronchogenic) Cysts (Clinically, Cystic Congenital Thoracic Malformations) Foregut cysts can be defined as closed epithelium-lined sacs developing abnormally in the thorax from the primitive developing upper gut and respiratory tract.
What is an esophageal duplication cyst?
Esophageal duplication cysts are rare inherited lesions usually diagnosed in early childhood. Most of them are found in the mediastinum and manifest themselves as separate masses along or in continuity with the native esophagus. Their prevalence remains unknown and they are treated either surgically or endoscopically.
Can a bronchogenic cyst be cancerous?
Although extremely rare, malignant transformation of a bronchogenic cyst is well known and has been reported in several cases.
How rare is a duplication cyst?
Gastric duplication cysts are a rare phenomenon and account for only 2–9% of all gastrointestinal duplications . The majority is circular, non-communicating and surrounded by a smooth muscular coat.
Should bronchogenic cysts be removed?
Surgical resection of bronchogenic cyst is often recommended, as the cyst can lead to complications including infection, hemorrhage, rupture and malignant degeneration if left untreated .
What causes bronchogenic cyst?
The causes of bronchogenic cyst are largely unknown, but thought to be an abnormal growth of the upper gastrointestinal and respiratory tract during fetal development. Bronchogenic cysts are not usually associated with genetic or chromosomal differences.
Are all esophageal tumors cancerous?
Sometimes a tumor develops in your esophagus that is not cancerous (benign). The most common type—representing about 70 percent of benign tumors—is leiomyoma, which forms in the muscle. Doctors do not know what causes benign esophageal tumors. When these tumors are small, you may not have any symptoms.
Can you have a benign tumor in your esophagus?
Leiomyoma. Leiomyoma is the most common type of non-cancerous tumour found in the esophagus. It starts in the smooth muscle cells and is usually found in the lower two-thirds of the esophagus. These are benign, slow growing tumours, but sometimes they can become cancerous.
What are the different types of duplication cysts?
Foregut duplication cysts are a type of congenital duplication cyst. They are sometimes classified under bronchopulmonary foregut malformations. Entities classified as foregut duplication cysts include: bronchogenic cysts. neurenteric cysts. other enteric cysts esophageal duplication cysts.
How old are the patients with foregut cysts?
Four of the foregut duplications involved the esophagus, and 5 involved the stomach. Three patients had thoracic cysts located in the posterior mediastinum. All 12 duplications were cystic. The patients’ ages at surgery were between 2 and 12 years, with a mean age of 7.2 years.
Can a radiograph show a gastric duplication cyst?
An abdominal plain radiograph can demonstrate a soft tissue mass displacing air-filled bowel loops. There can be occasional calcification in the cysts wall 6. A barium study may show a filling defect due to extrinsic compression from these cystic masses.
How many gastric duplication cysts are there in the world?
Gastric duplication cyst 1 Epidemiology. A review of four large series comprising 281 cases of gastrointestinal tract duplication cysts, demonstrated that duplications of the stomach constituted about 7% 1. 2 Clinical presentation. 3 Pathology. 4 Radiographic features. 5 Treatment and prognosis. 6 Differential diagnosis.