What is the life expectancy of a child with HLHS?

There are currently estimates of three- to five-year survival rates of 70% for infants who have the stage I repair. For children who survive to the age of 12 months, long-term survival is about 90 percent.

What is the survival rate of hypoplastic left heart syndrome?

Hospital survival rates reported are 94% to 98% following the hemi-Fontan procedure and 86% to 94% following the Fontan procedure (2,38–40). Actuarial survival for all infants with combined staged procedures has been reported to be 63% to 80% at one year of age and 58% to 72% at five years of age (2,39,41–43).

How long does babies with hypoplastic left heart stay in the hospital?

The length of hospital stay will vary. The average recovery time is 1-3 weeks. After surgery, the baby will go to the Cardiac Intensive Care Unit (CICU) and will have a chest tube and intravenous lines (IV’s).

How old is the oldest person with hypoplastic left heart syndrome?

The oldest living person with HLHS is their 30s.

Is HLHS worse than Hrhs?

HRHS is less common than Hypoplastic Left Heart Syndrome (HLHS), which is an underdevelopment of the left side of the heart. If your doctor suspects a fetal heart anomaly after reviewing your routine ultrasound, he or she may request a fetal echocardiogram (echo), an ultrasound of the fetus’s heart.

Is HLHS a rare disease?

Hypoplastic left heart syndrome is a rare disorder that affects males (67 percent) more often than females. The estimated prevalence of the disorder is 1 in 100,000 live births. Hypoplastic left heart syndrome accounts for 7-9 percent of all congenital heart defects.

Is Hlhs worse than Hrhs?

What are my chances of having another baby with hypoplastic left heart syndrome?

For example, in classical Hypoplastic Left Heart Syndrome the risk of having another child with Hypoplastic Left Heart Syndrome has been reported to be as high as 8% (8 in 100) although this has not been my personal experience and I have found the recurrence much less.

Can you survive HLHS?

It is fatal without surgical intervention and responsible for 25% to 40% of all neonatal cardiac mortality. Studies have shown 1-year survival for HLHS ranges from 20% to 60%,3–9 with relatively stable 5-year, 10-year, and 15-year survival of ∼40%.

Is HLHS genetic?

HLHS typically occurs sporadically (randomly), in otherwise normal babies with no family history of HLHS. In a few children, isolated HLHS is known to be genetic. These cases may be due to mutations in the GJA1 gene with autosomal recessive inheritance, or the NKX2-5 gene with autosomal dominant inheritance.

What are the chances of having a second baby with CHD?

Individuals who have a personal or family history of CHD have a higher chance of a heart defect happening again in the family. For most people, the risk of having another child with a congenital heart defect ranges from 3-5 percent. However, for those who have particularly rare conditions, the risk can go up to 50%.